Giant Cell Arteritis/Temporal Arteritis
Giant Cell Arteritis (GCA) is a systemic large-vessel vasculitis, typically affecting the temporal arteries (at temple region). It usually affects caucasian women > 50 years, and is very strongly associated with Polymyalgia Rheumatica.
Presentation
Temporal headache - severe and unilateral
Scalp tenderness e.g. when brushing/combing hair
Jaw claudication - pain/fatigue on chewing/prolonged speaking due to ischaemic supply to masseters
Vision loss, which is irreversible if not treated immediately
It's most commonly due to arteritis anterior ischaemic optic neuropathy (AAION), which is inflammation and subsequent ischaemia of the optic nerve.
It's less commonly due to central retinal artery occlusion (CRAO), which is ischaemia of the retina.
Complications
The main complication is Permanent vision loss. This is avoided by giving high-dose steroids immediately once suspected to prevent further progression of the vision loss.
Other complications include:
Stroke
Relapse
Aortic complications, including Aortic aneurysm and dissection
Investigations
Bloods - ESR, FBC
Temporal artery biopsy - This is needed for a definitive diagnosis. It will show multi-nucleated giant cells.
Management
Urgent referral to opthalmology
Start immediately on 40-60mg Prednisolone PO
Should be a major improvement after 45 mins
After good response, start on Reducing Regime
If symptoms recur while on reducing regime, you may need to increase dose or stay on dose longer before reducing again
N.B. Give Methylprednisolone 500-1000mg if vision loss on presentation.
Alongside steroids, the patients should be co-prescribed:
Bisphosphonates for bone protection
PPI for gastro protection
Low-dose Aspirin for risk of vision loss and stroke