Polycystic Kidney Disease (PKD)
Polycystic Kidney Disease (PKD) is a genetic condition, causing multiple cysts to form in kidneys, therefore significantly impairing its function. More commonly an autosomal dominant inheritance, but it can be autosomal recessive.
It's associated with Cerebral berry aneurysms. These most commonly form at the junction between the anterior communicating artery and anterior cerebral artery.
Hepatic cysts are its most common extra-renal manifestation.
Presents with:
HTN
Flank pain and haematuria with cyst rupture
Flank pain, fever and urinary symptoms with cyst infection
Investigations - Renal US
Management
Manage CKD and HTN
Tolvaptan (ADH receptor antagonist), which slows down cyst development and progression of renal decline
Complications
Cyst rupture
Cyst infection
CKD
Subarachnoid haemorrhage due to berry aneurysm
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